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Adult congenital heart disease: Anomalous pulmonary veins

Mayo Clinic adult congenital heart disease expert, Naser M. Ammash, M.D., discusses partial anomalous pulmonary venous connection (PAPVC). For more information or to request an appointment, visit here.

Anomalous pulmonary venous connections are a rare and simple congenital heart defect when they occur in isolation. However, in many patients, they are associated with other congenital heart diseases such as atrial septal defect or tetralogy of Fallot.

Transthoracic echocardiogram, transesophageal echocardiogram, CT scan, and MRI can all be used to identify anomalous pulmonary venous connections, and treatment can oftentimes require surgical repair.

Video content outline:

  • Introduction
  • What are anomalous pulmonary venous connections? (0:18)
  • When do you suspect PAPVC? (0:52)
  • Tools used to identify PAPVC (3:28)
  • Management or repair of anomalous pulmonary veins (7:38)
  • Anomalous pulmonary veins — Take-home message (8:56)
  • Conclusion (10:15)

Published

October 20, 2017

Created by

Mayo Clinic

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